Thalassemia in Children — Symptoms and Treatment
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چکیده
Thalassemias are a group of inherited disorders that are characterized by decreased production of the alpha or beta globin chains. The amount of the produced normal hemoglobin within the red blood cells correlates with the severity of the symptoms. Fetuses with alpha-thalassemia major usually die. Children with beta-thalassemia major are usually dependent on repeated blood transfusions. Splenectomy is the only therapeutic option that is known to result in improvement of symptoms and severity of the anemia in children with major thalassemia. Bone marrow transplantation is becoming a possible curative option for selected patients with beta-thalassemia major.
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